Chii chinonzi polydactyly uye nei zvichiitika?

zvigunwe tsoka

Polydactyly ishoko rechimiro chechiGiriki rinoreva minwe yakawanda. Icho chirwere chemagene umo munhu ane zvigunwe kupfuura zvakajairwa, zvishanu paruoko nerutsoka. Kazhinji mumwe munwe wekuwedzera, uyo unodanwa wakawedzera mimwe kana minwe inoshamisa.

Uyu deformation haina kukanganisa hutano hwemwana kana musikanakune iyo yainayo, kunyangwe mune dzimwe nguva, inogona kuve yakabatana neakakomba maitiro echisikigo, ayo anogona kuve nekumwe kukanganisa kwemuviri. Isu tinokuudza zvimwe zvimisikidzo nezve izvi zvisina kumira zvakanaka, zvakajairika kupfuura zvaunofunga.

Zvakajairika sei kuva ne polydactyly?

polydactyly tsoka

Kuzvarwa uine mimwe minwe kwakajairika, nhamba 1 mu500 vacheche vane polydactyly. Kunyange chiri chokwadi kuti mukana uyu unowedzera pakati pevaAmish kana vanhu vatema. Kumwe kuda kuziva, vakomana vakawanda vanozvarwa vaine minwe inodarika mishanu pane vasikana. Ruoko rwerudyi netsoka rekuruboshwe ndizvo zvinonyanya kutapurwa.

Kune atove mamiririri ekare umo izvi zvakasarudzika zvakaitika, umo munwe wekuwedzera uri mudiki pane vamwe vese. Kune mamwe makuhwa, kana ngano dzemumadhorobha dzinodaro Kim Kardashian, Marylin Monroe, kana Halle Berry, vese vaitofanira kuzviramba.

Postaxial polydactyly, inoitika kudivi re munwe mudiki kana chigunwe, kazhinji zvinomhanya mumhuri. Zvishoma kazhinji, zvinoitika pachigunwe kana pachigunwe chikuru chetsoka, uye kazhinji kacho, inogona kuve yepakati uye inoitika pakati pezvigunwe kana zvigunwe.

Iyo polydactyly inoonekwa sei uye kurapwa?

fetus

Mune Prenatal ultrasound inogona kutoona polydactyly. Kana ikasaonekwa mairi, mwana achangoberekwa, nyamukuta, amai vacho pachavo, pamusoro pechiremba, vachazviongorora nekukasira. Kazhinji yenguva, maX-ray anoitwa kuti aone kana chigunwe chekuwedzera chine mapfupa nemajoini. Izvi zvinobatsira chiremba anovhiya nezve kurapwa.

El Kurapa kunoenderana nekuti panowanikwa mumwe munwe, kana iri muruoko, mutsoka uye maumbirwo ayo. Kazhinji yenguva, mukukurukurirana kwekunze kwekunze, pamwe neinesthesia yemuno kana yemusoro, inogona kutemwa, kana ichibatanidzwa neponda rakapetana reganda. Nema stitches mashoma, ayo anozonyungudika mumavhiki maviri kana mana, "dambudziko" rapera. Uku kuvhiyiwa kunogona kupihwa semucheche, semwana, kana kunyangwe semunhu mukuru, kunatsiridza chitarisiko kana mashandiro.

Muzviitiko zvakawanda, hazvina kana basa kuti upfuure neiyi yekupindira, nekuti mwana anogona kudzora ruoko kana rutsoka basa chakakanganiswa pasina matambudziko. Imwe nzira yekurapa kwekuita basa, kurapa kwemuviri, kana kurovedza muviri kumba kunogona kudikanwa. Dzimwe nguva ine bhonzo risina majoini, uye zvakanyanya pano neapo munwe wakakwana uye unoshanda. Iyo kashoma kuzvarwa kubva pachiuno, mune ruoko, senge mimwe minwe.

Zvimwe zvinetso zvakakomba zvine chekuita neichi chisina kujairika

Kunetseka kwepfungwa

La syndromic polydactyly, iyo inosangana neimwe geni mamiriro. zvinogona kukonzera kudzikira mune zvimwe zvikamu zvemuviri. Inogona kusanganisira kukura kwakashata uye kukura pamwe nekuziva kuremara, kusagadzikana kwemusoro uye kumeso, zvinokonzerwa nechirwere chepasi.

Kuongororwa kwevanhu vanopfuura 5.900 XNUMX vanhu vane polydactyly kwakaratidza izvo chete 14,6% yavo vakaberekwa vaine chinobatanidza majini kusagadzikana. Sezvo genetics yakafambira mberi, subtypes akaiswa muzvikamu zvichienderana nekusiyana mukukanganisa uye majini anobatanidzwa.

Zvimwe zve dzakabatana magene syndromes vane polydactyly vane Down syndrome, vanobatana zvakanyanya nezvigunwe zviviri; Saethre-Chotzen syndrome inosanganisira kaviri yekutanga munwe. Kune rimwe divi, Bardet-Beidl syndrome inosanganisirwa ne polydactyly uye syndactyly muzvigunwe nezvigunwe, zvichingodaro nevamwe. Asi sezvatakambotaura pakutanga, syndromic polydactyly yakanyanya kushoma pane yakasarudzika polydactyly.


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  1. Inotarisira iyo data: Miguel Ángel Gatón
  2. Chinangwa cheiyo data: Kudzora SPAM, manejimendi manejimendi.
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