Ose November 13, iyo Zuva reInternational chirwere cheHuntington. Ichi chirwere chisingawanzo, chinouraya majini pathology inofambira mberi zvishoma nezvishoma uye zvishoma nezvishoma Chirwere cheHuntington chinogona kuitika muvana, chinoonekwa mumakore gumi ekutanga. Iko hakuna chaiyo data pane yavo kuwanda, nekuti iwo mashoma kashoma zviitiko.
Kana chirwere chacho anozviratidza muhudiki anozviita zvakasiyana kusvika pazvinoitika mumunhu mukuru, izvo zvinogona kutungamira mukusaziva. Tichabata nezvenyaya idzi nedzimwe nyaya nhasi muchinyorwa chino.
Chirwere cheHuntington chekutanga kwehucheche
Sechirwere che Huntington hudiki kutanga Chirwere cheHuntington chinozivikanwa muvana. Ichi chirwere chine genetic chikamu yakakosha kwazvo, kusvika padanho rekuti pasi rese pane tarisiro, mu mamwe matunhu, nemhuri dzakazara inobatwa nechirwere.
Kunyangwe pasina dhata chairo, zvinofungidzirwa kuti kutanga-kutanga kwechirwere cheHuntington, icho chinosanganisira zviitiko zvese zvinoratidza chirwere pamberi pemakore makumi maviri, inobata nezve 20% yevarwere vane chirwere ichi, asi hazvizivikanwe kuti vangani muzana muzana vane zviratidzo vasati vasvitsa makore gumi. Zvinotaridza kuti pane hukama hwakananga umo kutapurirana kunoitika kuburikidza nemutsara wababa.
Zvinosuruvarisa tarisiro yeupenyu yevana vaHuntington's kazhinji haipfuure makore gumi mushure mekutanga kwezviratidzo zvekutanga. Uye ndezvekuti nhasi hapana mushonga. MuUnited States, isu tichangobva kudzidza kuti FDA yakapa nherera kudomwa branaplan, iyo inoderedza huwandu hweprotein huntigtin, uye ichivhura nzira yetariro kumhuri.
Zviratidzo zveHuntington muvana
Kana chirwere ichi chikazviratidza muhudiki, chinozviita nehunhu hwakasiyana pane hwevakuru. Iyo zviratidzo zvekutanga muvana ivo vanowanzo kuve:
- Kugadziriswa kwekufunga. Dambudziko rekuwana hunyanzvi uye kugona kunoonekwa sematanho ezera ravo. Panogona kuve nekukundikana kwechikoro kana kurasikirwa kwehunyanzvi hwakawanikwa kare.
- Kuvhiringidzika kwemaitiro. Izvo zvinowanzoitika hasha, hunhu hunhu, uye kusagadzikana. Nekuda kwezviratidzo izvi, dzimwe nguva, kana nhoroondo yemhuri isingazivikanwe, panogona kunge paine nyonganiso mukuongororwa uye inobatwa seKutariswa Kusakwana Hyperactivity Disorder (ADHD).
vamwe zviratidzo zvisingawanzoitika, asi izvo zvinogona zvakare kumuka mangwanani:
- Kufenda kwakafanana neiko kunoitika kuvanhu vane pfari.
- Matambudziko nehunyanzvi hwemotokari.
- Gait kukanganiswa.
Sezvo chiri chirwere chinofambira mberi sezvo chirwere ichi chichifambira mberi ivo vachamuka vamwe, semuenzaniso:
- Rigidity
- Kushaya simba, kushaya simba mumakumbo
- Kufamba kusingaite kusazvibata
- Zvakaoma kududza mazwi
- Kumedza matambudziko
Iko kune kusarongeka kufamba kunoratidzira chirwere chaHuntington, inozivikanwa se Chorea yaHuntington hazvina kujairika kuti zvioneke sechiratidzo pakutanga kwechirwere. Muvana inoonekwa mumatanho epamberi, zvinopesana nezvinoitika muvakuru.
Kukahadzika kwemhuri kana paine zviitiko zveHuntington
Mumhuri dzine nhoroondo yechirwere cheHuntington, pane mubvunzo wekuti shanduko inogona kukanganisa kukura kwevana vavo munzira ipi neipi kana kutomuka sevana. Nyaya zhinji dzaHuntington hadziratidze muhucheche, uye mune iyi kesi mhuri ichaona kuti mwana ane hwakajairika hudiki, zvisingaenzanisike kubva kune zvevamwe vana.
Zvisinei, zvinokwanisika kuti vazhinji vevana ava vakaziva kana kukurira mudzimba dzavo pachavo nenhengo inorwara nechirwere ichi. Uye izvi zvine mhedzisiro padanho remanzwiro uye hupenyu hwezuva nezuva mumwana.
Kubva pakuona kwemasvomhu pane mishonga miviri yakatenderwa kurapwa kwechorea, asi isu tatozvitaura kare kuti chorea hachisi chiratidzo chikuru muvana vane chirwere cheHuntington. Kunze kwemishonga, mudiki achafanirwa kuchengetwa na neuropsychologists, physiotherapists, matarenda ekurapa nevamwe vanyanzvi vanozokubatsira nechiratidzo chekurapa chirwere ichi, uye nekupa hupenyu hwako hwepamoyo.